Prognostic factors indicating survival with native liver after Kasai procedure for biliary atresia

Pediatr Surg Int. 2017 Oct;33(10):1047-1052. doi: 10.1007/s00383-017-4135-y. Epub 2017 Aug 29.

Abstract

Background: The number of the bile ducts in the portal canal/measured surface area of the portal canal (BDP ratio) indicates prognosis in biliary atresia (BA), as does an elevated cytokeratin 7 positivity percentage (PCK7). We compared these two markers.

Methods: We reviewed 32 BA cases undergoing Kasai operation from 1976 to 2016 with >5 portal canals in biopsy samples. Group I required liver transplantation or died within a year of operation (n = 8). Group II survived with their native liver (n = 24). We determined the BDP ratio (102/mm2) and PCK7 (%), subdividing patients into three groups by their age at operation: Group A ≤60 days (n = 6, 1 Group I), 60< Group B ≤90days (n = 16, 5 Group I), Group C >90 days (n = 10, 2 Group I).

Results: PCK7 (%) was 2.71 ± 1.87 in Group I and 4.25 ± 2.56 in Group II (p = 0.13). BDP ratio (102/mm2) was 1.19 ± 0.424 in Group I and 1.64 ± 0.534 in Group II (p = 0.04). Both markers were higher in Group C than in Group A or B (p < 0.01).

Conclusion: The BDP ratio is a better prognostic indicator than PCK7 in BA.

Keywords: Biliary atresia; Prognosis; The bile ducts in portal canal; The cytokeratin 7 positivity percentage.

MeSH terms

  • Bile Ducts / pathology*
  • Biliary Atresia / blood
  • Biliary Atresia / pathology
  • Biliary Atresia / surgery*
  • Female
  • Humans
  • Infant
  • Keratin-7 / blood*
  • Liver / surgery
  • Male
  • Portoenterostomy, Hepatic / methods*
  • Prognosis
  • Survival Analysis

Substances

  • Keratin-7