Homozygous osteogenesis imperfecta unlinked to collagen I genes

Hum Genet. 1988 Mar;78(3):233-6. doi: 10.1007/BF00291667.

Abstract

In a consanguineous pedigree in which a severe type of osteogenesis imperfecta was segregating as an autosomal recessive trait, analysis of genetic markers for both collagen I structural loci COL1A1 and COL1A2 showed that the phenotype was unlinked to either locus.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Collagen / genetics*
  • Consanguinity
  • Genetic Linkage*
  • Genetic Markers
  • Homozygote*
  • Humans
  • Infant, Newborn
  • Male
  • Osteogenesis Imperfecta / diagnostic imaging
  • Osteogenesis Imperfecta / genetics*
  • Pedigree
  • Phenotype
  • Polymorphism, Restriction Fragment Length
  • Radiography

Substances

  • Genetic Markers
  • Collagen