c-Abl-mediated Drp1 phosphorylation promotes oxidative stress-induced mitochondrial fragmentation and neuronal cell death

Cell Death Dis. 2017 Oct 12;8(10):e3117. doi: 10.1038/cddis.2017.524.

Abstract

Oxidative stress-induced mitochondrial dysfunction and neuronal cell death have important roles in the development of neurodegenerative diseases. Dynamin related protein 1 (Drp1) is a critical factor in regulating mitochondrial dynamics. A variety of posttranslational modifications of Drp1 have been reported, including phosphorylation, ubiquitination, sumoylation and S-nitrosylation. In this study, we found that c-Abl phosphorylated Drp1 at tyrosine 266, 368 and 449 in vitro and in vivo, which augmented the GTPase activity of Drp1 and promoted Drp1-mediated mitochondrial fragmentation. Consistently, c-Abl-mediated phosphorylation is important for GTPase activity of Drp1 and mitochondrial fragmentation. Furthermore, we found that Drp1 phosphorylation mediated by c-Abl is required for oxidative stress-induced cell death in primary cortical neurons. Taken together, our findings reveal that c-Abl-Drp1 signaling pathway regulates oxidative stress-induced mitochondrial fragmentation and cell death, which might be a potential target for the treatment of neurodegenerative diseases.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Cell Death / physiology*
  • Cell Line
  • Dynamins / metabolism*
  • GTP Phosphohydrolases / metabolism
  • HEK293 Cells
  • Humans
  • Hydrogen Peroxide / pharmacology
  • Mice
  • Mice, Knockout
  • Mitochondria / pathology*
  • Mitochondrial Dynamics / physiology*
  • Neurodegenerative Diseases / pathology
  • Neurons / pathology
  • Oxidative Stress / physiology*
  • Phosphorylation
  • Proto-Oncogene Proteins c-abl / metabolism*

Substances

  • Hydrogen Peroxide
  • Proto-Oncogene Proteins c-abl
  • GTP Phosphohydrolases
  • Dnm1l protein, mouse
  • Dynamins