Near Complete Obliteration of the Left Hemithorax by Congenital Lobar Emphysema in an Adult

Ann Thorac Surg. 2017 Nov;104(5):e367-e369. doi: 10.1016/j.athoracsur.2017.06.068.

Abstract

Congenital lobar emphysema is a rare pulmonary malformation typically diagnosed during infancy and is characterized by bullous disease. A 28-year-old woman, who presented with 1 week of progressive dyspnea and chest pain, was found to have left hemithoracic lung hyperinflation with perfusion deficit upon radiographic evaluation. Bullous disease was found intraoperatively to originate from 1 lower lobe segment. Normal parenchymal lung expansion occurred following resection of the affected segment. Therefore, we present a rare case of congenital lobar emphysema resulting in near-complete occupancy of the left hemithorax and diagnosed in a previously asymptomatic adult without history of predisposing factors.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Bronchoscopy / methods
  • Chest Pain / diagnosis
  • Chest Pain / etiology
  • Disease Progression
  • Dyspnea / diagnosis
  • Dyspnea / etiology
  • Emergency Service, Hospital
  • Female
  • Follow-Up Studies
  • Humans
  • Pneumothorax / diagnostic imaging*
  • Pneumothorax / etiology
  • Pneumothorax / surgery
  • Positron-Emission Tomography / methods
  • Pulmonary Emphysema / complications
  • Pulmonary Emphysema / congenital*
  • Pulmonary Emphysema / diagnostic imaging
  • Pulmonary Emphysema / surgery
  • Radiography, Thoracic / methods
  • Rare Diseases
  • Risk Assessment
  • Severity of Illness Index
  • Thoracic Surgery, Video-Assisted / methods*
  • Tomography, X-Ray Computed / methods
  • Treatment Outcome

Supplementary concepts

  • Congenital lobar emphysema