Adult-onset Rasmussen encephalitis associated with focal cortical dysplasia

Epileptic Disord. 2017 Dec 1;19(4):476-480. doi: 10.1684/epd.2017.0947.

Abstract

Rasmussen encephalitis is a rare, devastating condition, typically presenting in childhood. Cases of adult-onset Rasmussen have also been described, but the clinical picture is less defined, rendering final diagnosis difficult. We present a case of adult-onset Rasmussen encephalitis with dual pathology, associated with focal cortical dysplasia and encephalitis. We interpreted the Rasmussen encephalitis to be caused by severe and continuous epileptic activity due to focal cortical dysplasia. The best therapeutic approach for such cases remains unclear.

Keywords: adult-onset Rasmussen encephalitis; dual pathology; focal cortical dysplasia.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Brain / diagnostic imaging*
  • Electroencephalography
  • Encephalitis / diagnostic imaging
  • Encephalitis / etiology*
  • Female
  • Humans
  • Magnetic Resonance Imaging
  • Malformations of Cortical Development / complications*
  • Malformations of Cortical Development / diagnostic imaging