Management of idiopathic spinal epidural lipomatosis: a case report and review of the literature

Childs Nerv Syst. 2018 Apr;34(4):757-763. doi: 10.1007/s00381-017-3706-5. Epub 2017 Dec 22.

Abstract

Background: Spinal epidural lipomatosis (SEL) is a rare pathologic growth of histologically normal unencapsulated adipose tissue in the epidural space. Although rare, SEL can compress the spinal cord or nerve roots causing myelopathy or radiculopathy. While SEL has been associated with long-term exposure to endogenous or exogenous steroids and obesity, idiopathic forms of SEL are much rarer.

Case report: In this report, we present the first case of SEL isolated to the cervical region compressing the spinal cord in a healthy, non-obese, preadolescent patient.

Conclusion: Idiopathic SEL in the pediatric population is a rare entity. This is the first case of epidural lipomatosis isolated to the cervical region in an adult or child patient. In refractory, symptomatic cases of idiopathic SEL, surgical decompression is often required.

Keywords: Cervical spine; Congenital; Lipoma; Spinal cord compression; Spinal epidural lipomatosis; Spine.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Adipose Tissue / pathology
  • Child
  • Disease Management*
  • Epidural Space / diagnostic imaging
  • Epidural Space / surgery
  • Female
  • Humans
  • Laminoplasty / methods*
  • Lipomatosis / diagnostic imaging
  • Lipomatosis / surgery*
  • Magnetic Resonance Imaging
  • Spinal Cord / diagnostic imaging
  • Spinal Cord / surgery*