Severe Craniofacial Involvement due to Amniotic Band Sequence

Fetal Pediatr Pathol. 2018 Feb;37(1):27-37. doi: 10.1080/15513815.2017.1392663. Epub 2018 Jan 16.

Abstract

Background: Disruptive amniotic band sequence (DABS) is a sporadic, non-familial disorder with unclear etiology. Diagnosis is based on clinical features because there is currently no reliable laboratory diagnostic tests.

Objective: We describe six cases of DABS with severe craniofacial deformations, three with and three without classical constrictive limb deformation.

Results: The craniofacial deformities were delimited by peripheral sharply demarcated scarring.

Conclusion: When a sharply demarcated linear disruptive craniofacial lesion is observed, DABS should be considered despite the absence of constrictive limb scarring.

Keywords: Amniotic band sequence; disruptive sequence; facial clefts; limb-body wall defects.

Publication types

  • Case Reports

MeSH terms

  • Amniotic Band Syndrome / complications*
  • Amniotic Band Syndrome / pathology*
  • Craniofacial Abnormalities / etiology*
  • Craniofacial Abnormalities / pathology*
  • Female
  • Humans
  • Infant
  • Infant, Newborn
  • Male

Supplementary concepts

  • Amniotic Band Sequence