Idiopathic hypertrophic pachymeningitis as a rare cause of cervical compressive myelopathy

J Craniovertebr Junction Spine. 2017 Oct-Dec;8(4):387-389. doi: 10.4103/jcvjs.JCVJS_118_17.

Abstract

The spinal form of idiopathic hypertrophic pachymeningitis (IHP) is a rare condition characterized by a chronic progressive diffuse inflammatory fibrosis of the dura mater, which may evolve to the compression of the spinal cord. We present a case report about IHP focusing on its features in magnetic resonance imaging, which are determined by an intradural extramedullary mass in the cervical spine showing hypointensity on T2-weighted images and peripheral enhancement, causing compression of the spinal cord. Histological analysis showed a nonspecific chronic inflammatory process in dense fibrous tissue. The patient had a good outcome after therapy with steroids.

Keywords: Idiopathic hypertrophic pachymeningitis; cervical spine; magnetic resonance imaging.

Publication types

  • Case Reports