[Intra-cardiac manifestation during adult-onset Still's disease's, a tricuspid vegetation as a rare expression of systemic disease]

Rev Med Interne. 2018 Oct;39(10):816-819. doi: 10.1016/j.revmed.2018.04.016. Epub 2018 May 3.
[Article in French]

Abstract

Introduction: Adult-onset Still's Disease is a rare multisystemic inflammatory disease characterized by fever, maculo-papular erythematous rash and arthralgia. Adult-onset Still's disease is a diagnosis of exclusion.

Case report: We report the case of a 33 years old man, hospitalized for fever, arthralgia and throat manifestations, leading to Adult-onset Stills's Disease diagnosis. Cardiac ultrasound revealed tricuspid vegetation. Once infectious causes were ruled out, the vegetation was related to Adult-onset Still's Disease according to Fautrel and Yamaguchi criteria. The patient was treated with systemic high doses corticosteroid and cardiac surgery. Histological examination excluded infection and neoplasia, and showed cruoric and fibrinous vegetation.

Conclusion: Non-infectious endocarditis, with a vegetation made of cruoric and fibrinous material, is a rare complication of Adult-onset Still's disease.

Keywords: Adult-onset Still's Disease (AODS); Corticoid; Corticothérapie; Endocardite non infectieuse; Endocarditis; Maladie auto-inflammatoire; Maladie de Still de l’adulte; Systemic auto-inflammatory disease; Tricuspid vegetation; Végétation tricuspidienne.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Endocarditis, Non-Infective / diagnosis*
  • Endocarditis, Non-Infective / etiology
  • Humans
  • Male
  • Still's Disease, Adult-Onset / complications*
  • Still's Disease, Adult-Onset / diagnosis*
  • Tricuspid Valve Insufficiency / diagnosis*
  • Tricuspid Valve Insufficiency / etiology