ERCC1-deficient cells and mice are hypersensitive to lipid peroxidation

Free Radic Biol Med. 2018 Aug 20:124:79-96. doi: 10.1016/j.freeradbiomed.2018.05.088. Epub 2018 Jun 1.

Abstract

Lipid peroxidation (LPO) products are relatively stable and abundant metabolites, which accumulate in tissues of mammals with aging, being able to modify all cellular nucleophiles, creating protein and DNA adducts including crosslinks. Here, we used cells and mice deficient in the ERCC1-XPF endonuclease required for nucleotide excision repair and the repair of DNA interstrand crosslinks to ask if specifically LPO-induced DNA damage contributes to loss of cell and tissue homeostasis. Ercc1-/- mouse embryonic fibroblasts were more sensitive than wild-type (WT) cells to the LPO products: 4-hydroxy-2-nonenal (HNE), crotonaldehyde and malondialdehyde. ERCC1-XPF hypomorphic mice were hypersensitive to CCl4 and a diet rich in polyunsaturated fatty acids, two potent inducers of endogenous LPO. To gain insight into the mechanism of how LPO influences DNA repair-deficient cells, we measured the impact of the major endogenous LPO product, HNE, on WT and Ercc1-/- cells. HNE inhibited proliferation, stimulated ROS and LPO formation, induced DNA base damage, strand breaks, error-prone translesion DNA synthesis and cellular senescence much more potently in Ercc1-/- cells than in DNA repair-competent control cells. HNE also deregulated base excision repair and energy production pathways. Our observations that ERCC1-deficient cells and mice are hypersensitive to LPO implicates LPO-induced DNA damage in contributing to cellular demise and tissue degeneration, notably even when the source of LPO is dietary polyunsaturated fats.

Keywords: 4-hydroxynonenal; Aging; DNA damage; ERCC1-XPF; Lipid peroxidation; Progeria; Senescence.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Cell Proliferation
  • Cellular Senescence*
  • DNA Damage*
  • DNA Repair*
  • DNA-Binding Proteins / physiology*
  • Endonucleases / physiology*
  • Lipid Peroxidation*
  • Mice
  • Mice, Knockout
  • Oxidative Stress*
  • Reactive Oxygen Species / metabolism

Substances

  • DNA-Binding Proteins
  • Reactive Oxygen Species
  • Endonucleases
  • Ercc1 protein, mouse