Mice harboring the human SLC30A8 R138X loss-of-function mutation have increased insulin secretory capacity

Proc Natl Acad Sci U S A. 2018 Aug 7;115(32):E7642-E7649. doi: 10.1073/pnas.1721418115. Epub 2018 Jul 23.

Abstract

SLC30A8 encodes a zinc transporter that is primarily expressed in the pancreatic islets of Langerhans. In β-cells it transports zinc into insulin-containing secretory granules. Loss-of-function (LOF) mutations in SLC30A8 protect against type 2 diabetes in humans. In this study, we generated a knockin mouse model carrying one of the most common human LOF mutations for SLC30A8, R138X. The R138X mice had normal body weight, glucose tolerance, and pancreatic β-cell mass. Interestingly, in hyperglycemic conditions induced by the insulin receptor antagonist S961, the R138X mice showed a 50% increase in insulin secretion. This effect was not associated with enhanced β-cell proliferation or mass. Our data suggest that the SLC30A8 R138X LOF mutation may exert beneficial effects on glucose metabolism by increasing the capacity of β-cells to secrete insulin under hyperglycemic conditions.

Keywords: SLC30A8; genetic mutation; insulin secretion; pancreatic beta cell; zinc transporter.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Alleles
  • Animals
  • Blood Glucose
  • Diabetes Mellitus, Type 2 / genetics*
  • Diabetes Mellitus, Type 2 / metabolism
  • Disease Models, Animal
  • Gene Knock-In Techniques
  • Glucose / metabolism*
  • Humans
  • Hyperglycemia / blood
  • Hyperglycemia / chemically induced
  • Hyperglycemia / metabolism
  • Insulin / metabolism*
  • Insulin Secretion
  • Insulin-Secreting Cells / metabolism*
  • Loss of Function Mutation
  • Male
  • Mice
  • Mice, Inbred C57BL
  • Mice, Knockout
  • Peptides / pharmacology
  • Receptor, Insulin / antagonists & inhibitors
  • Receptor, Insulin / metabolism
  • Zinc Transporter 8 / genetics*
  • Zinc Transporter 8 / metabolism

Substances

  • Blood Glucose
  • Insulin
  • Peptides
  • S961 peptide
  • SLC30A8 protein, human
  • Slc30a8 protein, mouse
  • Zinc Transporter 8
  • Receptor, Insulin
  • Glucose