The authors performed a nationwide study in Japan to evaluate the annual detected rate of pediatric intracranial arteriovenous (AV) shunts such as brain AV malformations (BAVMs), pial AV fistulas (PAVFs), vein of Galen aneurysmal malformations (VGAMs), and dural AV fistulas (DAVFs). These rates were revealed for the first time and showed that VGAM, DAVF, and PAVF were relatively common but that BAVMs were extremely rare in neonates and infants.
Keywords: ADR = annual detected rate; AV = arteriovenous; BAOS = Bicêrtre Admission and Outcome Score; BAVM = brain AV malformation; BNES = Bicêrtre Neonatal Evaluation Score; DAVF = dural AV fistula; JPAS = Japanese Pediatric Arteriovenous Shunts Study; Japanese population; PAVF = pial AV fistula; TAE = transarterial embolization; TVE = transvenous embolization; VGAM = vein of Galen aneurysmal malformation; brain arteriovenous shunt; incidence; pediatric vascular disease; vascular disorders.