Mortality in autoimmune rheumatic diseases with anti-Ro/SSA antibody in Korea: Single center-based retrospective study

Int J Rheum Dis. 2019 Feb;22(2):191-199. doi: 10.1111/1756-185X.13430. Epub 2018 Nov 5.

Abstract

Aim: The clinical importance of the anti-Ro antibody has not been completely understood. This study investigated identification of the association between mortality and clinical features in patients with autoimmune rheumatic diseases and detectable anti-Ro antibody titers.

Methods: We retrospectively analyzed a total of 336 patients with autoimmune rheumatic diseases and positive anti-Ro antibody titers from January 2012 to January 2015. Clinical manifestations and other autoantibodies detected during the follow-up period were identified. Cumulative survival rates were assessed by Kaplan-Meier analysis. Differences between survival curves for each risk factor were analyzed by log-rank test. The relative risk of mortality was assessed using standardized mortality ratios (SMRs).

Results: There was no difference in the mortality rates of patients with autoimmune rheumatic diseases with or without detectable anti-Ro antibody (SMR: 1.373, 95% CI: 0.539-2.791). Six patients (4 with systemic lupus erythematosus [SLE] and two with Sjögren's syndrome [SS]) died during the follow-up period. In the whole study population, the mortality rate of patients with lymphopenia was higher than those without lymphopenia (P = 0.023). In a sub-group of patients with both SLE and SS, Kaplan-Meier analysis showed that lymphopenia and interstitial lung disease were associated with increased mortality (P = 0.024 and P = 0.023, respectively).

Conclusion: This study demonstrated that presence of the anti-Ro antibody was not associated with increased mortality in patients with autoimmune rheumatic disease. Conversely, we found that lymphopenia was independently associated with mortality in patients with autoimmune rheumatic disease.

Keywords: Sjögren’s syndrome; anti-Ro antibody; mortality; systemic lupus erythematosus.

Publication types

  • Comparative Study

MeSH terms

  • Adult
  • Antibodies, Antinuclear / blood*
  • Autoimmune Diseases / blood
  • Autoimmune Diseases / diagnosis
  • Autoimmune Diseases / immunology
  • Autoimmune Diseases / mortality*
  • Biomarkers / blood
  • Female
  • Humans
  • Lymphopenia / immunology
  • Lymphopenia / mortality
  • Male
  • Middle Aged
  • Predictive Value of Tests
  • Prognosis
  • Republic of Korea / epidemiology
  • Retrospective Studies
  • Rheumatic Diseases / blood
  • Rheumatic Diseases / diagnosis
  • Rheumatic Diseases / immunology
  • Rheumatic Diseases / mortality*
  • Risk Factors
  • Serologic Tests
  • Time Factors

Substances

  • Antibodies, Antinuclear
  • Biomarkers
  • SS-A antibodies