Novel mutation in CCBE 1 as a cause of recurrent hydrops fetalis from Hennekam lymphangiectasia-lymphedema syndrome-1

Clin Case Rep. 2018 Oct 24;6(12):2358-2363. doi: 10.1002/ccr3.1804. eCollection 2018 Dec.

Abstract

Whole exome sequencing (WES) was used to determine the etiology of recurrent hydrops fetalis in this case of Hennekam lymphangiectasia-lymphedema syndrome-1. WES is a useful approach for diagnosing rare single-gene conditions with nonspecific phenotypes and should be considered early in the diagnostic process of investigating fetal abnormalities.

Keywords: Hennekam syndrome; congenital abnormalities; exome sequencing; genetic testing; hydrops fetalis; prenatal diagnosis.

Publication types

  • Case Reports