Therapeutic Effects of Short Cyclic and Combined Epitope Peptides in a Long-Term Model of Graves' Disease and Orbitopathy

Thyroid. 2019 Feb;29(2):258-267. doi: 10.1089/thy.2018.0326.

Abstract

Background: Cyclic peptides derived from some cylindrical loops of the leucine-rich repeat domain (LRD) of the thyrotropin receptor (TSHR) have been shown to treat disease manifestations in a mouse model of Graves' disease during a long-term protocol of four-weekly immunizations with adenovirus coding for the TSHR A-subunit (Ad-TSHR289).

Methods: In a follow-up study, two additional cyclic peptides were tested, which were shortened in order to obtain additional information on the minimally involved epitopes and to enable easier production conditions. In addition, a linear peptide was tested, which mimics parts of three loops of the native TSHR LRD structure, and is potentially able to block the discontinuous epitopes of anti-TSHR antibodies.

Results: The novel peptides markedly reduced thyroid size, serum thyroxine levels, retro-orbital fibrosis, and tachycardia in Ad-TSHR289-immunized mice. In immunologically naïve mice, administration of the peptides did not induce any immune response.

Conclusions: In summary, novel cyclic peptides mitigate many clinical findings in a mouse model of established Graves' disease and orbitopathy, and may therefore provide an additional therapeutic option compared to existing drugs or interventions.

Keywords: Graves' disease; autoimmunity; peptides; thyroid.

MeSH terms

  • Adenoviridae
  • Animals
  • Disease Models, Animal
  • Epitopes / chemistry
  • Female
  • Fibrosis
  • Graves Ophthalmopathy / immunology*
  • Graves Ophthalmopathy / therapy
  • HEK293 Cells
  • Humans
  • Immunoglobulins, Thyroid-Stimulating
  • Mice
  • Mice, Inbred BALB C
  • Orbit / physiopathology*
  • Peptides, Cyclic / therapeutic use*
  • Receptors, Thyrotropin / genetics
  • Tachycardia / genetics
  • Thyroxine / blood

Substances

  • Epitopes
  • Immunoglobulins, Thyroid-Stimulating
  • Peptides, Cyclic
  • Receptors, Thyrotropin
  • TSHR protein, human
  • Thyroxine