Dynamic inosinome profiles reveal novel patient stratification and gender-specific differences in glioblastoma

Genome Biol. 2019 Feb 13;20(1):33. doi: 10.1186/s13059-019-1647-x.

Abstract

Background: Adenosine-to-inosine (A-to-I) RNA editing is an essential post-transcriptional mechanism mediated by ADAR enzymes that have been recently associated with cancer.

Results: Here, we characterize the inosinome signature in normal brain and de novo glioblastoma (GBM) using new metrics that re-stratify GBM patients according to their editing profiles and indicate this post-transcriptional event as a possible molecular mechanism for sexual dimorphism in GBM. We find that over 85% of de novo GBMs carry a deletion involving the genomic locus of ADAR3, which is specifically expressed in the brain. By analyzing RNA editing and patient outcomes, an intriguing gender-dependent link appears, with high editing of Alus shown to be beneficial only in male patients. We propose an inosinome-based molecular stratification of GBM patients that identifies two different GBM subgroups, INO-1 and INO-2, which can identify novel high-risk gender-specific patient groups for which more aggressive treatments may be necessary.

Conclusions: Our data provide a detailed picture of RNA editing landscape in normal brain and GBM, exploring A-to-I RNA editing regulation, disclosing unexpected editing implications for GBM patient stratification and identification of gender-dependent high-risk patients, and suggesting COG3 I/V as an eligible site for future personalized targeted gene therapy.

Keywords: ADAR; COG3; GBM; RNA editing; RNA-Seq.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adaptor Proteins, Vesicular Transport / genetics
  • Adenosine Deaminase / metabolism*
  • Age Factors
  • Alu Elements
  • Astrocytes / metabolism
  • Brain / metabolism
  • Brain Neoplasms / genetics*
  • Brain Neoplasms / metabolism
  • Brain Neoplasms / mortality
  • Case-Control Studies
  • Cell Line, Tumor
  • Glioblastoma / genetics*
  • Glioblastoma / metabolism
  • Glioblastoma / mortality
  • HEK293 Cells
  • Humans
  • Inosine / metabolism*
  • RNA Editing*
  • Sex Factors

Substances

  • Adaptor Proteins, Vesicular Transport
  • COG3 protein, human
  • Inosine
  • Adenosine Deaminase