Auditory Neuropathy: Bridging the Gap Between Hearing Aids and Cochlear Implants

Otolaryngol Clin North Am. 2019 Apr;52(2):349-355. doi: 10.1016/j.otc.2018.11.016. Epub 2019 Feb 12.

Abstract

Auditory neuropathy spectrum disorder (ANSD) is a complex and heterogeneous disorder associated with altered neural synchrony with respect to auditory stimuli. Patients have characteristic auditory findings including normal otoacoustic emissions in the setting of abnormal auditory brainstem response. Patients with ANSD have a high incidence of comorbid developmental delay that may impact speech outcomes. Treatment options for ANSD include hearing amplification and cochlear implantation. The article highlights issues and controversies with the diagnosis and treatment of this complex disorder.

Keywords: Auditory neuropathy spectrum disorder; Cochlear implant; Hearing aid; Hearing loss.

Publication types

  • Review

MeSH terms

  • Cochlear Implants*
  • Hearing Aids*
  • Hearing Loss, Central / diagnosis
  • Hearing Loss, Central / therapy*
  • Hearing Tests
  • Humans
  • Speech Perception

Supplementary concepts

  • Auditory neuropathy