[A case of Erdheim-Chester disease]

J J Liang; Q H Li; Y Q Mo; X N Wei; D H Zheng; L Dai

doi:10.3760/cma.j.issn.0578-1426.2019.03.013

[A case of Erdheim-Chester disease]

Zhonghua Nei Ke Za Zhi. 2019 Mar 1;58(3):215-217. doi: 10.3760/cma.j.issn.0578-1426.2019.03.013.

[Article in Chinese]

Authors

J J Liang¹, Q H Li, Y Q Mo, X N Wei, D H Zheng, L Dai

Affiliation

¹ Department of Rheumatology, Sun Yat-Sen Memorial Hospital, Sun Yat-Sen University, Guangzhou 510120, China.

PMID: 30803182
DOI: 10.3760/cma.j.issn.0578-1426.2019.03.013

Abstract

Erdheim-Chester病（Erdheim-Chester disease，ECD）是一种罕见的非朗格汉斯细胞组织细胞增生症，其临床表现异质性高，从无症状骨病变到危及生命的多脏器功能衰竭均可出现。本文报道1例以全身骨痛、心包积液、肺内结节为主要表现并经骨骼病理确诊的ECD，经干扰素α治疗后患者全身骨痛缓解且C反应蛋白水平下降。.