Evidence for BCR/ABL1-positive T-cell acute lymphoblastic leukemia arising in an early lymphoid progenitor cell

Pediatr Blood Cancer. 2019 Sep;66(9):e27829. doi: 10.1002/pbc.27829. Epub 2019 May 28.

Abstract

BCR-ABL1-positive leukemias have historically been classified as either chronic myelogenous leukemia or Ph+ acute lymphoblastic leukemia. Recent analyses suggest there may be a wider range of subtypes. We report a patient with BCR-ABL1 fusion positive T-cell ALL with a previously undescribed cell distribution of the fusion gene. The examination of sorted cells by fluorescence in situ hybridization showed the BCR-ABL1 fusion in the malignant T cells and a subpopulation of the nonmalignant B cells, but not nonmalignant T cells or myeloid or CD34+ progenitor cells providing evidence that the fusion may have occurred in an early lymphoid progenitor.

Keywords: BCR-ABL1; T-cell ALL; discordant MRD.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Flow Cytometry
  • Fusion Proteins, bcr-abl* / genetics
  • Fusion Proteins, bcr-abl* / metabolism
  • Humans
  • In Situ Hybridization
  • Lymphoid Progenitor Cells* / enzymology
  • Lymphoid Progenitor Cells* / pathology
  • Male
  • Precursor T-Cell Lymphoblastic Leukemia-Lymphoma* / enzymology
  • Precursor T-Cell Lymphoblastic Leukemia-Lymphoma* / genetics
  • Precursor T-Cell Lymphoblastic Leukemia-Lymphoma* / pathology

Substances

  • BCR-ABL1 fusion protein, human
  • Fusion Proteins, bcr-abl