Molecular genetic and immunohistochemical analyses of a case of multicentric Castleman's disease

Jpn J Clin Oncol. 1988 Jun;18(2):149-57.

Abstract

Whether Castleman's disease is primarily hyperplastic or neoplastic in nature is a matter of controversy; however, the classical localized form has been thought clinically benign in itself, because it can be cured by local therapy. Recently, a multicentric form of the disease has been reported and has received attention because of its aggressive clinical course and high incidence of developing malignant lymphoma. Here, we describe a case of multicentric Castleman's disease which occurred in a 24-year-old Japanese man. To ascertain whether a monoclonal population was present or not, we performed a molecular genetic analysis of the genes encoding the T-cell receptor and the immunoglobulin, as well as a conventional immunohistochemical analysis. Using these sensitive methods, no monoclonal population could be found. The findings suggest that our case represents a reactive rather than a neoplastic disorder.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Antigens, Neoplasm / analysis
  • Antigens, Surface / analysis
  • Castleman Disease / diagnosis
  • Castleman Disease / genetics*
  • DNA, Neoplasm / analysis
  • Genes, Immunoglobulin*
  • Genes, MHC Class II*
  • Humans
  • Immunoglobulin Constant Regions / genetics
  • Immunoglobulin Heavy Chains / genetics
  • Immunoglobulin Joining Region / genetics
  • Immunohistochemistry
  • Male
  • Neoplasms, Multiple Primary / diagnosis
  • Neoplasms, Multiple Primary / genetics*
  • Receptors, Immunologic / genetics

Substances

  • Antigens, Neoplasm
  • Antigens, Surface
  • DNA, Neoplasm
  • Immunoglobulin Constant Regions
  • Immunoglobulin Heavy Chains
  • Immunoglobulin Joining Region
  • Receptors, Immunologic