Complement activation products in the circulation and urine of primary membranous nephropathy

BMC Nephrol. 2019 Aug 9;20(1):313. doi: 10.1186/s12882-019-1509-5.

Abstract

Background: Complement activation plays a substantial role in the pathogenesis of primary membranous nephropathy (pMN). C5b-9, C3c, MBL, and factor B have been documented in the subepithelial immune deposits. However, the changing of complement activation products in circulation and urine is not clear.

Methods: We measured the circulating and urinary levels of C1q, MBL, C4d, Bb, properdin, C3a, C5a, and sC5b-9, in 134 patients with biopsy-proven pMN, by enzyme-linked immunosorbent assay. All the plasma values were corrected by eGFR and all the urinary values were corrected by urinary creatinine and urinary protein excretion. Anti-PLA2R antibodies were measured in all patients.

Results: The plasma complement activation products were elevated both in the patients with and without anti-PLA2R antibodies. C3a levels were remarkably increased in the circulation and urine, much higher than the elevated levels of C5a. C5b-9 was in normal range in plasma, but significantly higher in urine. The urinary C5a had a positive correlation with anti-PLA2R antibody levels and urinary protein. The plasma level of C4d was elevated, but C1q and MBL were comparable to healthy controls. Positive correlations were observed between plasma C4d/MBL and urinary protein, only in the patients with positive anti-PLA2R antibodies but not in those without. The plasma level of Bb was elevated and had positive correlation with urinary protein only in the patients without anti-PLA2R antibodies.

Conclusion: Complement activation products were remarkable increased in pMN and may serve as sensitive biomarkers of disease activity. The complement may be activated through lectin pathway with the existence of anti-PLA2R antibodies, while through alternative pathway in the absence of antibody.

Keywords: C3a; C5a; Complement; PLA2R; Primary membranous nephropathy.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Adult
  • Aged
  • Aged, 80 and over
  • Case-Control Studies
  • Complement Activation*
  • Complement C1q / analysis
  • Complement C1q / urine
  • Complement C3a / analysis
  • Complement C3a / urine
  • Complement C4 / analysis
  • Complement C4 / urine
  • Complement C5a / analysis
  • Complement C5a / urine
  • Complement Factor B / analysis
  • Complement Factor B / urine
  • Complement Membrane Attack Complex / analysis
  • Complement Membrane Attack Complex / urine
  • Complement System Proteins / analysis*
  • Complement System Proteins / urine
  • Creatinine / blood
  • Creatinine / urine
  • Female
  • Glomerulonephritis, Membranous / blood*
  • Glomerulonephritis, Membranous / immunology
  • Glomerulonephritis, Membranous / therapy
  • Glomerulonephritis, Membranous / urine*
  • Humans
  • Male
  • Mannose-Binding Lectin / blood
  • Mannose-Binding Lectin / urine
  • Middle Aged
  • Properdin / analysis
  • Properdin / urine
  • Receptors, Phospholipase A2 / analysis
  • Receptors, Phospholipase A2 / blood
  • Receptors, Phospholipase A2 / immunology
  • Regression Analysis
  • Statistics, Nonparametric
  • Young Adult

Substances

  • Complement C4
  • Complement Membrane Attack Complex
  • Mannose-Binding Lectin
  • PLA2R1 protein, human
  • Receptors, Phospholipase A2
  • Properdin
  • Complement C1q
  • Complement C3a
  • Complement C5a
  • Complement System Proteins
  • Creatinine
  • Complement Factor B