Electrical storm in an acquired short QT syndrome successfully treated with quinidine

Michael Spartalis; Efthimios Livanis; Eleftherios Spartalis; Alexandros Tsoutsinos

doi:10.1002/ccr3.2282

Electrical storm in an acquired short QT syndrome successfully treated with quinidine

Clin Case Rep. 2019 Jun 23;7(8):1617-1618. doi: 10.1002/ccr3.2282. eCollection 2019 Aug.

Authors

Michael Spartalis¹, Efthimios Livanis¹, Eleftherios Spartalis², Alexandros Tsoutsinos³

Affiliations

¹ Division of Cardiology Onassis Cardiac Surgery Center Athens Greece.
² Laboratory of Experimental Surgery and Surgical Research, Medical School University of Athens Athens Greece.
³ Department of Pediatric Cardiology & Adult Congenital Heart Disease Onassis Cardiac Surgery Center Athens Greece.

Abstract

Short QT syndrome (SQTS) is a malignant heart disorder defined by the presence of ventricular arrhythmias causing syncope and sudden cardiac arrest. The prevalence in the pediatric population is 0.05%. Quinidine is an established agent for pharmacological prophylaxis in SQTS patients, but can also terminate an electrical storm.

Keywords: arrhythmia; electrical storm; quinidine; short QT.