Moyamoya disease is a rare angiopathy characterized by a progressive distal occlusion of the internal carotid arteries and their branches. Extracerebral involvement, including coronary arteries, has been described. We report the case of a patient with moyamoya disease who suffered an out-of-hospital cardiac arrest associated with coronary spasm. We discussed the possible links between coronary spasm and moyamoya, as well as the contribution of multimodal cardiac imaging, combining conventional and intracoronary imaging, cardiac MRI, provocative tests for spasm, in the exploration of out-of-hospital cardiac arrest without obvious electrocardiographic and angiographic cause.
Keywords: Angor spastique; Arrêt cardiaque; Coronary spasm; Moyamoya; Out-of-hospital cardiac arrest; Prinzmetal; Variant angina.
Copyright © 2019 Elsevier Masson SAS. All rights reserved.