Duplication of atrioventricular valves involves the mitral valve more often than the tricuspid valve and is often associated with other cardiac defects. Double-orifice tricuspid valve (DOTV) is often identified in surgery or autopsy and missed on echocardiography, as the two orifices are orthogonal to the imaging plane. If suspected on echocardiography, it masquerades as mild tricuspid hypoplasia. Three-dimensional echocardiography and magnetic resonance imaging of a DOTV are presented.
Keywords: Double-orifice tricuspid valve; duplication of atrioventricular valves; magnetic resonance imaging; three-dimensional echocardiography; tricuspid hypoplasia; ventricular septal defect.