[Respiratory care for children with spinal muscular atrophy]

Zhonghua Er Ke Za Zhi. 2019 Oct 2;57(10):810-812. doi: 10.3760/cma.j.issn.0578-1310.2019.10.018.
[Article in Chinese]

Abstract

脊髓性肌萎缩症是一种常见的遗传性神经肌肉病，临床表现为肢体近端进行性对称性肌无力和肌萎缩，常可累及呼吸系统，导致患儿出现呼吸困难、夜间低通气以及反复肺炎。呼吸道管理对于脊髓性肌萎缩症患儿至关重要。本文就目前国外关于脊髓性肌萎缩症患儿呼吸道管理相关文献进行综述，以期为国内致力于该疾病治疗的临床工作者提供理论支持。.

Publication types

  • Review

MeSH terms

  • Child
  • Humans
  • Muscular Atrophy, Spinal / complications*
  • Muscular Atrophy, Spinal / diagnosis
  • Muscular Atrophy, Spinal / therapy*
  • Respiratory Insufficiency / etiology
  • Respiratory Insufficiency / physiopathology
  • Respiratory Insufficiency / therapy*
  • Respiratory Paralysis / etiology
  • Respiratory Paralysis / physiopathology
  • Respiratory Paralysis / therapy*
  • Treatment Outcome