Glomus tumors are tumors that arise from the glomus bodies, which can be found in sites of arteriovenous anastomosis. Glomus tumors can occur in all parts of the body but rarely occur in the trachea. The PET/CT findings of these tumors are similar to those of malignant tracheal tumors. We reported the PET/CT findings of a pathologically proven primary glomus tumor in the trachea of a 41-year-old man.