Pediatric pulmonary lymphatic flow Disorders: Diagnosis and management

Paediatr Respir Rev. 2020 Nov:36:2-7. doi: 10.1016/j.prrv.2019.11.002. Epub 2019 Nov 29.

Abstract

Pulmonary lymphatic flow disorders involve the abnormal lymphatic flow via lymphatic channels to the lungs and pleural space. Plastic bronchitis and chylothorax are the main complications of this abnormal lymphatic perfusion, which has been termed pulmonary lymphatic perfusion syndrome (PLPS). Following lymphatic access, dynamic contrast MR lymphangiography is the imaging modality of choice to diagnose these disorders. Management includes medical therapy, percutaneous interventions under fluoroscopy, and surgical interventions.

Keywords: Children; Chylothorax; Lymphangiography; Plastic bronchitis.

Publication types

  • Review

MeSH terms

  • Adolescent
  • Bronchitis / diagnostic imaging*
  • Bronchitis / therapy
  • Child
  • Child, Preschool
  • Chylothorax / diagnostic imaging*
  • Chylothorax / therapy
  • Contrast Media
  • Diet Therapy
  • Dietary Supplements
  • Disease Management
  • Embolization, Therapeutic
  • Humans
  • Infant
  • Lung Diseases / diagnostic imaging
  • Lung Diseases / therapy
  • Lymphatic Abnormalities / diagnostic imaging
  • Lymphatic Abnormalities / therapy
  • Lymphatic Diseases / diagnostic imaging
  • Lymphatic Diseases / therapy
  • Lymphatic Vessels / abnormalities
  • Lymphatic Vessels / diagnostic imaging*
  • Lymphatic Vessels / surgery
  • Lymphography*
  • Magnetic Resonance Imaging*
  • Microsurgery

Substances

  • Contrast Media