A rare case report of bilateral recurrent inguinal hernia due to persistent Müllerian duct syndrome treated by transabdominal preperitoneal repair

Medicine (Baltimore). 2020 Feb;99(7):e19079. doi: 10.1097/MD.0000000000019079.

Abstract

Introduction: Persistent Müllerian duct syndrome (PMDS) is a rare disease occurring in men with an otherwise completely normal phenotype, in which female internal sex organs are present, including a uterus, fallopian tubes, cervix, and vagina. We report a case of bilateral recurrent inguinal hernia due to PMDS treated by transabdominal preperitoneal repair (TAPP).

Patient concerns: A 72-year-old male presented with a complaint of swelling on both sides of the groin. The patient had undergone bilateral inguinal hernia suture repair 50 years ago.

Diagnosis: Bilateral recurrent inguinal hernia INTERVENTIONS:: TAPP was performed. There was a fibrous structure linking the left and right hernia orifice and a muscular structure in the hernia sac on the left. We noticed that the muscular structure was a vagina and fibrous structure was the salpinx, and we diagnosed the patient with PMDS. Supravaginal hysterectomy and right salpingectomy were performed. After that a preperitoneal mesh repair was performed for bilateral inguinal hernia.

Outcomes: Histologically, the diagnosis was confirmed as PMDS. The patient had an uneventful recovery.

Conclusion: This case is the first case of bilateral recurrent inguinal hernia due to PMDS managed by TAPP.

Publication types

  • Case Reports

MeSH terms

  • Aged
  • Disorder of Sex Development, 46,XY / diagnosis*
  • Disorder of Sex Development, 46,XY / surgery*
  • Hernia, Inguinal / surgery*
  • Herniorrhaphy / instrumentation
  • Humans
  • Hysterectomy, Vaginal
  • Male
  • Recurrence
  • Salpingectomy
  • Surgical Mesh
  • Treatment Outcome

Supplementary concepts

  • Persistent Mullerian duct syndrome