[Ultra high-risk refractory multiple myeloma with a complex karyotype including t(14;19)]

Rinsho Ketsueki. 2020;61(3):240-244. doi: 10.11406/rinketsu.61.240.
[Article in Japanese]

Abstract

A 78-year-old man was hospitalized because of rapid progression of chronic renal failure and diagnosed with multiple myeloma (MM) IgG-λ type ISS-III R-ISS-II with complex karyotype including t(14;19). Even after receiving bortezomib-based regimens, his renal failure progressed. He became dependent on dialysis, which was required three times a week. After introducing the daratumumab (DARA)-based regimen, his renal function improved, the frequency of dialysis decreased to twice a week, and the free light chain (FLC) ratio also improved. However, his myeloma eventually followed a refractory course; therefore, pomalidomide (POM)-dexamethasone (Pd) regimen was administered. Pd regimen had a marked effect and normalized the FLC ratio after three courses of the treatment. However, his myeloma reprogressed with multiple extramedullary masses and he became del(17p) positive; eventually, he died on the 470th day of disease. MM with t(14;19) is rare and has a poor prognosis with a highly aggressive course; however, early introduction of DARA or POM may provide long-term response.

Keywords: Daratumumab; Multiple myeloma; Pomalidomide; t(14;19).

Publication types

  • Case Reports

MeSH terms

  • Aged
  • Antineoplastic Combined Chemotherapy Protocols
  • Bortezomib
  • Chromosomes, Human, Pair 14
  • Chromosomes, Human, Pair 19
  • Dexamethasone
  • Humans
  • Karyotype
  • Male
  • Multiple Myeloma* / genetics
  • Thalidomide

Substances

  • Thalidomide
  • Bortezomib
  • Dexamethasone