Glycerol Phenylbutyrate Therapy in Progressive Familial Intrahepatic Cholestasis Type 2

J Pediatr Gastroenterol Nutr. 2020 Jun;70(6):e139-e140. doi: 10.1097/MPG.0000000000002713.

Authors

Marion Almes^{1

2}, Agathe Jobert³, Martine Lapalus², Elodie Mareux², Emmanuel Gonzales^{1

2}, Emmanuel Jacquemin^{1

2}

Affiliations

¹ Pediatric Hepatology and Liver Transplantation Unit, National Reference Centre for Biliary Atresia and Genetic Cholestasis, FILFOIE, ERN RARE LIVER, Bicêtre Hospital, Assistance Publique - Hôpitaux de Paris, University Paris-Saclay, Le Kremlin-Bicêtre.
² Inserm U1193, Hepatinov, University Paris-Saclay, Orsay.
³ Pediatric Unit, Saint Nazaire Hospital, Saint Nazaire, France.

PMID: 32443059
DOI: 10.1097/MPG.0000000000002713

No abstract available

Publication types

Letter
Research Support, Non-U.S. Gov't

MeSH terms

Cholestasis, Intrahepatic* / drug therapy
Cholestasis, Intrahepatic* / genetics
Glycerol / analogs & derivatives
Humans
Phenylbutyrates

Substances

Phenylbutyrates
Glycerol
glycerol phenylbutyrate

Supplementary concepts

Cholestasis, progressive familial intrahepatic 1