Congenital superior vena cava (SVC) stenosis and obstructed supracardiac total anomalous pulmonary venous connection (TAPVC)-A surgical perspective

Sachin Mahajan; Sudhansoo Khanna; Manojkumar Rohit; Nirupam S Chakraborty; Ankit Singhal

doi:10.1111/jocs.14792

Congenital superior vena cava (SVC) stenosis and obstructed supracardiac total anomalous pulmonary venous connection (TAPVC)-A surgical perspective

J Card Surg. 2020 Sep;35(9):2399-2402. doi: 10.1111/jocs.14792. Epub 2020 Jul 27.

Authors

Sachin Mahajan¹, Sudhansoo Khanna¹, Manojkumar Rohit², Nirupam S Chakraborty¹, Ankit Singhal¹

Affiliations

¹ Department of Cardiovascular and Thoracic Surgery, Post Graduate Institute of Medical Education and Research (PGIMER), Chandigarh, India.
² Department of Cardiology, Post Graduate Institute of Medical Education and Research (PGIMER), Chandigarh, India.

PMID: 32720344
DOI: 10.1111/jocs.14792

Abstract

Congenital superior vena cava (SVC) stenosis is a very rare anomaly, especially in pediatric population. Coexistence with obstructed supracardiac total anomalous pulmonary venous connection (TAPVC) has never been reported. Clinical examination should prompt detailed and focused evaluation for this treatable etiology. Pericardial patch augmentation can cure SVC stenosis, and may allow for growth potential as well. We describe a case of congenital SVC stenosis in a case of obstructed supracardiac TAPVC in a 3-month-old infant, managed successfully.

Keywords: congenital; superior vena cava stenosis; supracardiac TAPVC.

Publication types

Case Reports

MeSH terms

Child
Constriction, Pathologic
Heart Defects, Congenital*
Humans
Infant
Pulmonary Veins* / diagnostic imaging
Pulmonary Veins* / surgery
Scimitar Syndrome* / diagnostic imaging
Scimitar Syndrome* / surgery
Vena Cava, Superior / diagnostic imaging
Vena Cava, Superior / surgery