Ebstein's anomaly of tricuspid valve with aortic stenosis and coarctation of aorta: Successful single-stage repair of a rare adult congenital heart disease

J Card Surg. 2020 Nov;35(11):3160-3165. doi: 10.1111/jocs.15004. Epub 2020 Sep 16.

Abstract

Ebstein's anomaly of the tricuspid valve is infrequently associated with left heart anomalies. The association of aortic stenosis in Ebstein's anomaly has been reported to be extremely rare and the association of coarctation of aorta is even rarer especially in adults. The combination of all three of these lesions is virtually unknown without any references in literature. We report here an unusual case of Ebstein's anomaly of the tricuspid valve and severe aortic stenosis with coarctation of aorta in an adult who presented to us with exertional dyspnoea in the third decade and underwent a successful single-stage intracardiac repair.

Keywords: Ebstein's; aortic stenosis; bicuspid; coarctation.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Aortic Coarctation / complications
  • Aortic Coarctation / surgery*
  • Aortic Valve Stenosis / complications
  • Aortic Valve Stenosis / surgery*
  • Cardiovascular Surgical Procedures / methods*
  • Dyspnea / etiology
  • Ebstein Anomaly / complications
  • Ebstein Anomaly / surgery*
  • Humans
  • Male
  • Rare Diseases / surgery*
  • Severity of Illness Index
  • Treatment Outcome
  • Tricuspid Valve / abnormalities*
  • Tricuspid Valve / surgery*
  • Young Adult