Dermatofibrosarcoma protuberans (DFSP) in children: A combined multidisciplinary approach

Pediatr Dermatol. 2021 Jan;38(1):233-236. doi: 10.1111/pde.14425. Epub 2020 Nov 11.

Abstract

Dermatofibrosarcoma protuberans (DFSP) is rare, comprising (1%-6%) of all sarcomas. The incidence is less than one per million before the age of 20. It is a locally aggressive tumor with a low risk of metastasis. We share our experience in the management of three pediatric patients with complex cases of DFSP in a combined surgical approach involving plastic and dermatologic surgery, using the slow Mohs micrographic surgery technique.

Keywords: cutaneous surgery; dermatofibrosarcoma; dermatopathology; neoplasms; skin.

Publication types

  • Case Reports

MeSH terms

  • Child
  • Dermatofibrosarcoma* / surgery
  • Humans
  • Mohs Surgery
  • Neoplasm Recurrence, Local / surgery
  • Sarcoma*
  • Skin Neoplasms* / surgery