Introduction: Scrotal lymphedema is a rare condition, with significant psychological and functional disability. To date, association with giant congenital melanocytic nevus has not been reported.
Case report: We report a case of a 15-year-old male with a giant congenital nevus associated with giant scrotal lymphedema. Surgical debulking with penoscrotoplasty achieved satisfactory functional and esthetic results.
Conclusions: Early diagnosis and surgical intervention should be advocated for congenital causes of large scrotal swelling.
Keywords: Lymphedema; Reconstruction; Scrotal; Scrotoplasty.
© 2020 The Authors. Published by Elsevier Ltd on behalf of British Association of Plastic, Reconstructive and Aesthetic Surgeons.