The C-degron pathway eliminates mislocalized proteins and products of deubiquitinating enzymes

EMBO J. 2021 Apr 1;40(7):e105846. doi: 10.15252/embj.2020105846. Epub 2021 Jan 20.

Abstract

Protein termini are determinants of protein stability. Proteins bearing degradation signals, or degrons, at their amino- or carboxyl-termini are eliminated by the N- or C-degron pathways, respectively. We aimed to elucidate the function of C-degron pathways and to unveil how normal proteomes are exempt from C-degron pathway-mediated destruction. Our data reveal that C-degron pathways remove mislocalized cellular proteins and cleavage products of deubiquitinating enzymes. Furthermore, the C-degron and N-degron pathways cooperate in protein removal. Proteome analysis revealed a shortfall in normal proteins targeted by C-degron pathways, but not of defective proteins, suggesting proteolysis-based immunity as a constraint for protein evolution/selection. Our work highlights the importance of protein termini for protein quality surveillance, and the relationship between the functional proteome and protein degradation pathways.

Keywords: C-degron pathway; CRL2 ubiquitin ligase; N-degron pathway; protein spatial quality control; protein termini.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Amino Acid Motifs
  • Cell Line, Tumor
  • HEK293 Cells
  • Humans
  • Protein Transport
  • Proteolysis*
  • Proteome / chemistry
  • Proteome / metabolism
  • Receptors, Cytokine / metabolism
  • Ubiquitination*

Substances

  • CRLF2 protein, human
  • Proteome
  • Receptors, Cytokine