A case of aggressive systemic mastocytosis with bulky lymphadenopathy showing response to midostaurin

Clin Case Rep. 2020 Dec 29;9(2):978-982. doi: 10.1002/ccr3.3717. eCollection 2021 Feb.

Abstract

Management of systemic mastocytosis is an emerging challenge which requires a multidisciplinary diagnostic approach and personalized treatment strategy. Midostaurin can rapidly reduce the disease burden, also in cladribine refractory cases.

Keywords: bulky lymphadenopathy; midostaurin; purine analogue; systemic mastocytosis.

Publication types

  • Case Reports