Mitochondrial NADP(H) generation is essential for proline biosynthesis

Science. 2021 May 28;372(6545):968-972. doi: 10.1126/science.abd5491. Epub 2021 Apr 22.

Abstract

The coenzyme nicotinamide adenine dinucleotide phosphate (NADP+) and its reduced form (NADPH) regulate reductive metabolism in a subcellularly compartmentalized manner. Mitochondrial NADP(H) production depends on the phosphorylation of NAD(H) by NAD kinase 2 (NADK2). Deletion of NADK2 in human cell lines did not alter mitochondrial folate pathway activity, tricarboxylic acid cycle activity, or mitochondrial oxidative stress, but rather led to impaired cell proliferation in minimal medium. This growth defect was rescued by proline supplementation. NADK2-mediated mitochondrial NADP(H) generation was required for the reduction of glutamate and hence proline biosynthesis. Furthermore, mitochondrial NADP(H) availability determined the production of collagen proteins by cells of mesenchymal lineage. Thus, a primary function of the mitochondrial NADP(H) pool is to support proline biosynthesis for use in cytosolic protein synthesis.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Cell Line
  • Cell Line, Tumor
  • Cell Proliferation
  • Citric Acid Cycle
  • Collagen / metabolism
  • Culture Media
  • Cytosol / metabolism
  • Female
  • Folic Acid / metabolism
  • Gene Knockout Techniques
  • Glutamic Acid / metabolism
  • Glutathione / metabolism
  • Humans
  • Metabolome
  • Mice
  • Mice, Nude
  • Mitochondria / metabolism*
  • Mitochondrial Proteins / genetics
  • Mitochondrial Proteins / metabolism*
  • NADP / metabolism*
  • Oxidative Stress
  • Phosphotransferases (Alcohol Group Acceptor) / genetics
  • Phosphotransferases (Alcohol Group Acceptor) / metabolism*
  • Proline / biosynthesis*

Substances

  • Culture Media
  • Mitochondrial Proteins
  • Glutamic Acid
  • NADP
  • Collagen
  • Folic Acid
  • Proline
  • NADK2 protein, human
  • Phosphotransferases (Alcohol Group Acceptor)
  • Glutathione