A Fatal Case of Toxic Epidermal Necrolysis Combined With Vanishing Bile Duct Syndrome and Hemophagocytic Lymphohistiocytosis

J Burn Care Res. 2021 Sep 30;42(5):1043-1046. doi: 10.1093/jbcr/irab058.

Abstract

This case report describes a case of fatal toxic epidermal necrolysis complicated by both vanishing bile duct syndrome and hemophagocytic lymphohistiocytosis due to Influenza B infection. Here we highlight the potential for complex morbidity secondary to underlying autoimmune hypersensitivity. Furthermore, the stepwise progression of these pathologies is noted, with the initial epidermal lesions first progressing to cholestatic injury and then subsequently to the hematologic manifestations.

Publication types

  • Case Reports

MeSH terms

  • Bile Duct Diseases / chemically induced*
  • Burns / pathology*
  • Fatal Outcome
  • Humans
  • Lymphohistiocytosis, Hemophagocytic / pathology*
  • Male
  • Stevens-Johnson Syndrome / pathology*