Multifocal Osteonecrosis in a 3-Year-old Child With Sickle Beta Plus Thalassemia

J Pediatr Hematol Oncol. 2022 Mar 1;44(2):e428-e430. doi: 10.1097/MPH.0000000000002155.

Abstract

Sickle beta+thalassemia is considered to be a mild form of sickle cell disease. However, some patients with mild disease can present with osteonecrosis. Here, we present a rare 3-year-old male who presented with acute pain, a baseline hemoglobin of 13 g/dL, who acutely developed multifocal osteonecrosis, and improved with partial exchange transfusion and hydroxyurea therapy.

Publication types

  • Case Reports

MeSH terms

  • Anemia, Sickle Cell* / complications
  • Anemia, Sickle Cell* / therapy
  • Child, Preschool
  • Humans
  • Hydroxyurea / therapeutic use
  • Male
  • Osteonecrosis* / etiology
  • Thalassemia* / complications
  • Thalassemia* / therapy
  • beta-Thalassemia* / complications
  • beta-Thalassemia* / therapy

Substances

  • Hydroxyurea