α-Synuclein A53T Binds to Transcriptional Adapter 2-Alpha and Blocks Histone H3 Acetylation

Int J Mol Sci. 2021 May 20;22(10):5392. doi: 10.3390/ijms22105392.

Abstract

α-Synuclein (α-syn) is a hallmark amyloidogenic protein component of Lewy bodies in dopaminergic neurons affected by Parkinson's disease (PD). Despite the multi-faceted gene regulation of α-syn in the nucleus, the mechanism underlying α-syn crosstalk in chromatin remodeling in PD pathogenesis remains elusive. Here, we identified transcriptional adapter 2-alpha (TADA2a) as a novel binding partner of α-syn using the BioID system. TADA2a is a component of the p300/CBP-associated factor and is related to histone H3/H4 acetylation. We found that α-syn A53T was more preferentially localized in the nucleus than the α-syn wild-type (WT), leading to a stronger disturbance of TADA2a. Indeed, α-syn A53T significantly reduced the level of histone H3 acetylation in SH-SY5Y cells; its reduction was also evident in the striatum (STR) and substantia nigra (SN) of mice that were stereotaxically injected with α-syn preformed fibrils (PFFs). Interestingly, α-syn PFF injection resulted in a decrease in TADA2a in the STR and SN of α-syn PFF-injected mice. Furthermore, the levels of TADA2a and acetylated histone H3 were significantly decreased in the SN of patients with PD. Therefore, histone modification through α-syn A53T-TADA2a interaction may be associated with α-syn-mediated neurotoxicity in PD pathology.

Keywords: Parkinson’s disease; histone acetylation; neurotoxicity; transcriptional adapter 2-alpha; α-synuclein.

MeSH terms

  • Acetylation
  • Animals
  • Cell Line, Tumor
  • Corpus Striatum / metabolism
  • DNA-Binding Proteins / metabolism*
  • Disease Models, Animal
  • Dopaminergic Neurons / metabolism
  • Histones / metabolism*
  • Humans
  • Lewy Bodies / metabolism
  • Male
  • Mice
  • Mice, Inbred C57BL
  • Nerve Degeneration / metabolism
  • Parkinson Disease / metabolism
  • Substantia Nigra / metabolism
  • Transcription Factors / metabolism*
  • alpha-Synuclein / metabolism*

Substances

  • DNA-Binding Proteins
  • Histones
  • Tada2a protein, mouse
  • Transcription Factors
  • alpha-Synuclein