Subglottic Mass as Isolated Manifestation of Relapsing Polychondritis at Presentation

Ear Nose Throat J. 2023 Sep;102(9):NP440-NP445. doi: 10.1177/01455613211016718. Epub 2021 Jun 3.

Abstract

Relapsing polychondritis (RP) is a rare systemic disease that is characterized by recurrent episodic inflammation of the cartilaginous structures of the body, resulting in their progressive destruction and subsequent replacement with fibrotic scar. We present a case of RP that initially manifested with subglottic involvement and we propose an innovative strategy for the treatment for laryngeal RP in phase of active inflammation. A multidisciplinary approach (rheumatologist, otolaryngologist, immunologist, internist, cardiologist, etc) and adequate follow-up are essential. The timeliness of the diagnosis is fundamental to contain the destructive effects on the cartilages involved.

Keywords: corticosteroid therapy; dysphonia; dyspnea; polychondritis; subglottic mass; systemic autoimmune disease.

Publication types

  • Case Reports

MeSH terms

  • Humans
  • Inflammation
  • Larynx*
  • Polychondritis, Relapsing* / complications
  • Polychondritis, Relapsing* / diagnosis
  • Polychondritis, Relapsing* / therapy
  • Rare Diseases