Blastic plasmacytoid dendritic cell neoplasm with cutaneous presentation: A case series in children

Pediatr Dermatol. 2021 Jul;38(4):883-886. doi: 10.1111/pde.14652. Epub 2021 Jun 22.

Abstract

Blastic plasmacytoid dendritic cell neoplasm (BPDCN) is a rare, aggressive hematologic malignancy that can present with multiorgan involvement including the skin. While this entity accounts for 0.1% of all cutaneous lymphomas in adults, fewer than 90 pediatric cases have been described in the literature. We present three cases of pediatric BPDCN, highlighting the variable cutaneous and clinical presentation.

Keywords: neoplasm-malignant; skin signs of systemic disease; therapy-systemic.

Publication types

  • Case Reports

MeSH terms

  • Child
  • Dendritic Cells
  • Hematologic Neoplasms*
  • Humans
  • Skin
  • Skin Neoplasms*