Short-term effect of elexacaftor-tezacaftor-ivacaftor on lung function and transplant planning in cystic fibrosis patients with advanced lung disease

J Cyst Fibros. 2021 Sep;20(5):768-771. doi: 10.1016/j.jcf.2021.05.009. Epub 2021 Jun 23.
No abstract available

Publication types

  • Multicenter Study
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Aminophenols / therapeutic use*
  • Benzodioxoles / therapeutic use*
  • Chloride Channel Agonists / therapeutic use
  • Cohort Studies
  • Cystic Fibrosis / drug therapy*
  • Cystic Fibrosis / physiopathology*
  • Cystic Fibrosis / surgery
  • Drug Therapy, Combination
  • Female
  • Humans
  • Indoles / therapeutic use*
  • Lung Transplantation
  • Male
  • Pyrazoles / therapeutic use*
  • Pyridines / therapeutic use*
  • Pyrrolidines / therapeutic use*
  • Quinolones / therapeutic use*
  • Respiratory Function Tests
  • Retrospective Studies

Substances

  • Aminophenols
  • Benzodioxoles
  • Chloride Channel Agonists
  • Indoles
  • Pyrazoles
  • Pyridines
  • Pyrrolidines
  • Quinolones
  • tezacaftor
  • ivacaftor
  • elexacaftor