Introduction and importance: The ossifying fibromyxoid tumor of soft tissue is a rare tumor of intermediate differentiation and uncertain lineage that occurs in adults mostly in the extremities and the trunk.
Presentation of case: we present a case of 57 year-old man presenting with a right scapular mass. It was a subcutaneous and painless mass that was largely excised. The diagnosis of ossifying fibromyxoid tumor of the right shoulder was made. The follow up of 1 year was without recurrence and metastasis.
Clinical discussion: The ossifying fibromyxoid tumor of soft tissue is exceptional, microscopic diagnosis and management is challenging, considering the scarcity of the tumor.
Conclusion: More cases and retrospective studies are needed to understand the pathogenesis and to determine optimal treatment regimens.
Keywords: Case report; EMA, Epithelial Membrane Antigen; EMNST, epithelioid malignant nerve sheath tumors; GFAP, Glial fibrillary acidic protein; Intermediate differentiation; OFT, ossifying fibromyxoid tumor; Ossifying fibromyxoid tumor; Pathology; SEF, sclerosing epithelioid fibrosarcoma; SMA, Smooth Muscle Actin; Soft tissue.
© 2021 The Authors.