Ossifying fibromyxoid tumor of soft tissue: A case report with review of literature

Ann Med Surg (Lond). 2021 Jun 9:67:102479. doi: 10.1016/j.amsu.2021.102479. eCollection 2021 Jul.

Abstract

Introduction and importance: The ossifying fibromyxoid tumor of soft tissue is a rare tumor of intermediate differentiation and uncertain lineage that occurs in adults mostly in the extremities and the trunk.

Presentation of case: we present a case of 57 year-old man presenting with a right scapular mass. It was a subcutaneous and painless mass that was largely excised. The diagnosis of ossifying fibromyxoid tumor of the right shoulder was made. The follow up of 1 year was without recurrence and metastasis.

Clinical discussion: The ossifying fibromyxoid tumor of soft tissue is exceptional, microscopic diagnosis and management is challenging, considering the scarcity of the tumor.

Conclusion: More cases and retrospective studies are needed to understand the pathogenesis and to determine optimal treatment regimens.

Keywords: Case report; EMA, Epithelial Membrane Antigen; EMNST, epithelioid malignant nerve sheath tumors; GFAP, Glial fibrillary acidic protein; Intermediate differentiation; OFT, ossifying fibromyxoid tumor; Ossifying fibromyxoid tumor; Pathology; SEF, sclerosing epithelioid fibrosarcoma; SMA, Smooth Muscle Actin; Soft tissue.

Publication types

  • Case Reports