Genomic Chaos (Multiple Copy Number Variations and Structural Reorganization) Detected in Two Prenatal Cases

Cytogenet Genome Res. 2021;161(5):236-242. doi: 10.1159/000515653. Epub 2021 Jul 16.

Abstract

The use of new technologies in the routine diagnosis of constitutional abnormalities, such as high-resolution chromosomal microarray and next-generation sequencing, has unmasked new mechanisms for generating structural variation of the human genome. For example, complex chromosome rearrangements can originate by a chromosome catastrophe phenomenon in which numerous genomic rearrangements are apparently acquired in a single catastrophic event. This phenomenon is named chromoanagenesis (from the Greek "chromo" for chromosome and "anagenesis" for rebirth). Herein, we report 2 cases of genomic chaos detected at prenatal diagnosis. The terms "chromothripsis" and "chromoanasynthesis" and the challenge of genetic counseling are discussed.

Keywords: Array CGH; Chromoanasynthesis; Chromothripsis; Prenatal diagnosis.

Publication types

  • Case Reports

MeSH terms

  • Abortion, Eugenic
  • Adult
  • Chromosome Breakpoints*
  • Chromothripsis*
  • Comparative Genomic Hybridization
  • DNA Copy Number Variations
  • Female
  • Fetus
  • Gene Rearrangement*
  • Genetic Counseling / ethics
  • Genome, Human*
  • High-Throughput Nucleotide Sequencing
  • Humans
  • Karyotyping / methods
  • Male
  • Pregnancy
  • Prenatal Diagnosis / methods*