Multiple molecular abnormalities in Ph1 chromosome positive acute lymphoblastic leukaemia

Br J Haematol. 1987 Nov;67(3):319-24. doi: 10.1111/j.1365-2141.1987.tb02353.x.

Abstract

The Ph1 chromosome is present in 95% of patients with chronic myelogenous leukaemia (CML). The Ph1 chromosome also occurs in 5-25% of children and adults with acute lymphoblastic leukaemia (ALL). This observation raises questions as to whether these diseases are similar or identical. In patients with CML the c-abl and bcr genes are translocated and abnormally expressed. We studied molecular events related to bcr and c-abl in five patients with ALL to determine its relationship to CML. Four had the Ph1 chromosome; the fifth a probable Ph1 chromosome. c-abl and bcr abnormalities identical to CML were detected in four suggesting a common molecular basis. One patient with the Ph1 chromosome and c-abl translocation lacked these molecular changes but had abnormal c-abl gene transcription apparently unrelated to bcr. These data suggest that Ph1 chromosome positive ALL is heterogeneous; in some patients the molecular abnormality is identical to CML; in others c-abl is likewise involved but via a different mechanism.

Publication types

  • Comparative Study

MeSH terms

  • Adolescent
  • Adult
  • Child
  • Child, Preschool
  • Chromosome Aberrations*
  • DNA / genetics
  • Female
  • Humans
  • Leukemia, Lymphoid / genetics*
  • Leukemia, Myeloid / genetics
  • Male
  • Philadelphia Chromosome
  • Transcription, Genetic
  • Translocation, Genetic

Substances

  • DNA