Protein-losing enteropathy managed with percutaneous enlargement of a restrictive atrial septal defect

Milan Djukic; Stefan A Djordjevic; Andrija S Pavlovic; Igor Stefanovic; Mirko Topalovic; Ingo Dähnert

doi:10.1016/j.repce.2021.11.005

Protein-losing enteropathy managed with percutaneous enlargement of a restrictive atrial septal defect

Rev Port Cardiol (Engl Ed). 2021 Nov;40(11):895.e1-895.e4. doi: 10.1016/j.repce.2021.11.005.

Authors

Milan Djukic¹, Stefan A Djordjevic², Andrija S Pavlovic¹, Igor Stefanovic¹, Mirko Topalovic¹, Ingo Dähnert³

Affiliations

¹ Department of Cardiology, University Children's Hospital, Belgrade, Serbia.
² Department of Cardiology, University Children's Hospital, Belgrade, Serbia. Electronic address: [email protected].
³ Department of Pediatric Cardiology, Heart Center Leipzig, Leipzig, Germany.

PMID: 34857165
DOI: 10.1016/j.repce.2021.11.005

Abstract

Protein-losing enteropathy is one of the most feared complications of the Fontan circulation. The diagnosis of protein-losing enteropathy in this setting should prompt a thorough investigation for the presence of a treatable hemodynamic impairment. In this report, we describe a complete reversal of protein-losing enteropathy following percutaneous enlargement of a restrictive atrial septal defect in a patient with a fenestrated lateral tunnel Fontan and severe mitral stenosis.

Keywords: Atrial septum; Cardiac catheterization; Cateterismo cardíaco; Double outlet right ventricle; Dupla saída do ventrículo direito; Enteropatia por perda de proteínas; Estenose mitral; Fontan procedure; Mitral stenosis; Procedimento de Fontan; Protein-losing enteropathy; Septo auricular.

Publication types

Case Reports

MeSH terms

Fontan Procedure*
Heart Septal Defects, Atrial* / surgery
Hemodynamics
Humans
Postoperative Complications
Protein-Losing Enteropathies* / etiology