Novel and founder variants of SERPINA12 in Chinese patients with autosomal recessive palmoplantar keratoderma

Br J Dermatol. 2022 Aug;187(2):267-270. doi: 10.1111/bjd.21064. Epub 2022 May 6.

Abstract

1. We extend the spectrum of SERPINA12 variants in palmoplantar keratodermas. 2. The recurrent variant c.970_971del, mainly prevalent in the East Asia population, was proved to be a founder variant. 3. Considerable SERPINA12-related palmoplantar keratoderma patients could be identified from autosomal recessive, non-mutilating, diffused palmoplantar keratoderma patients. 4. Other serpin family members or their co-effect may participate in the etiologies of underexplored hereditary palmoplantar keratodermas.

Publication types

  • Letter

MeSH terms

  • China
  • Founder Effect
  • Humans
  • Keratoderma, Palmoplantar* / genetics
  • Serpins* / genetics

Substances

  • SERPINA12 protein, human
  • Serpins