Wisconsin syndrome with brain volume laterality: a case report and review of the literature

J Med Case Rep. 2022 Apr 16;16(1):153. doi: 10.1186/s13256-022-03332-8.

Abstract

Background: Wisconsin syndrome is a congenital anomaly caused by a 3q interstitial deletion. It is associated with characteristic facies and developmental delays. Only 33 cases with a deletion estimated to be in the associated region 3q25 have been reported.

Case report: We present the case of a 5-year-old Japanese girl with a 3q24q25.2 deletion. Her facial features corresponded to the Wisconsin syndrome phenotype, and she exhibited brain volume laterality, which has not been reported previously.

Conclusion: The clinical features of our case may contribute to narrowing down the list of candidate genes of Wisconsin syndrome.

Keywords: 3q interstitial deletion; Brain volume laterality; WWTR1; Wisconsin syndrome.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Brain / diagnostic imaging
  • Chromosome Aberrations*
  • Chromosome Deletion*
  • Facies
  • Female
  • Humans
  • Phenotype
  • Syndrome
  • Wisconsin