Hyperphosphorylated tau self-assembles into amorphous aggregates eliciting TLR4-dependent responses

Nat Commun. 2022 May 16;13(1):2692. doi: 10.1038/s41467-022-30461-x.

Abstract

Soluble aggregates of the microtubule-associated protein tau have been challenging to assemble and characterize, despite their important role in the development of tauopathies. We found that sequential hyperphosphorylation by protein kinase A in conjugation with either glycogen synthase kinase 3β or stress activated protein kinase 4 enabled recombinant wild-type tau of isoform 0N4R to spontaneously polymerize into small amorphous aggregates in vitro. We employed tandem mass spectrometry to determine the phosphorylation sites, high-resolution native mass spectrometry to measure the degree of phosphorylation, and super-resolution microscopy and electron microscopy to characterize the morphology of aggregates formed. Functionally, compared with the unmodified aggregates, which require heparin induction to assemble, these self-assembled hyperphosphorylated tau aggregates more efficiently disrupt membrane bilayers and induce Toll-like receptor 4-dependent responses in human macrophages. Together, our results demonstrate that hyperphosphorylated tau aggregates are potentially damaging to cells, suggesting a mechanism for how hyperphosphorylation could drive neuroinflammation in tauopathies.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Glycogen Synthase Kinase 3 beta / metabolism
  • Heparin
  • Humans
  • Phosphorylation
  • Protein Aggregation, Pathological / metabolism
  • Protein Isoforms / metabolism
  • Tauopathies* / metabolism
  • Toll-Like Receptor 4* / metabolism
  • tau Proteins* / metabolism
  • tau Proteins* / ultrastructure

Substances

  • Protein Isoforms
  • TLR4 protein, human
  • Toll-Like Receptor 4
  • tau Proteins
  • Heparin
  • Glycogen Synthase Kinase 3 beta